Review of primary and secondary erythromelalgia
نویسندگان
چکیده
منابع مشابه
Primary erythromelalgia: a review
Primary erythromelalgia (PE ORPHA90026) is a rare autosomal dominant neuropathy characterized by the combination of recurrent burning pain, warmth and redness of the extremities. The incidence rate of PE ranges from 0.36 to 1.1 per 100,000 persons. Gender ratio differs according to different studies and no evidence showed a gender preference. Clinical onset of PE is often in the first decade of...
متن کاملPrimary erythromelalgia: case report.
Erythromelalgia is a rare clinical syndrome characterized by heat, redness and intermittent pain in the extremities, being most frequent the bilateral development in the lower extremities. Local cooling brings relief to symptoms, while heating, physical exercises and use of stockings/socks intensify the discomfort. This condition can be primary or idiopathic or secondary to haematological disor...
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Erythromelalgia is a rare neurovascular pain syndrome characterized by a triad of redness, increased temperature, and burning pain primarily in the extremities. Erythromelalgia can present as a primary or secondary form, and secondary erythromelalgia associated with a myeloproliferative disease such as essential thrombocythemia often responds dramatically to aspirin therapy, as in the present c...
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Sternal tumors are very rare and challenging. Secondary sternal tumors are more common than primary tumors. These tumors are usually refractory to chemotherapy and radiotherapy, and surgery is the best choice for their treatment. In this study, we reported the collected data of 15 patients with primary and secondary tumors of the sternum, histological type, as well as kind of resection and reco...
متن کاملDual Effect of Ziconotide in Primary Erythromelalgia
Erythromelalgia (EM) is a rare disabling clinical syndrome more commonly known to affect the lower extremities. There is no single effective treatment for this disease that often requires a multidisciplinary approach. Herein, we report the case of a 31-year-old woman affected by primary erythromelalgia who was successfully treated with intrathecal Ziconotide. We also observed an unexpected resu...
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ژورنال
عنوان ژورنال: Clinical and Experimental Dermatology
سال: 2019
ISSN: 0307-6938,1365-2230
DOI: 10.1111/ced.13891